Home About us Current issue Ahead of Print Back issues Submission Instructions Advertise Contact Login   

Search Article 
  
Advanced search 
 
Saudi Journal of Kidney Diseases and Transplantation
Users online: 736 Home Bookmark this page Print this page Email this page Small font sizeDefault font size Increase font size 

CASE REPORT Table of Contents   
Year : 2021  |  Volume : 32  |  Issue : 1  |  Page : 223-226
A Rare Cause of Nephrotic Syndrome in Adults – Collagenofibrotic Glomerulopathy


1 Department of Nephrology, K S Hegde Medical Academy, Mangalore, Karnataka, India
2 Department of Pathology, K S Hegde Medical Academy, Mangalore, Karnataka, India

Correspondence Address:
Pradeep Shenoy
Department of Nephrology, K S Hegde Medical Academy, Mangalore, Karnataka
India
Login to access the Email id


DOI: 10.4103/1319-2442.318528

PMID: 34145135

Rights and Permissions

Adult-onset nephrotic syndrome (NS) is commonly caused by minimal change disease, focal segmental glomerulosclerosis, andmembranous nephropathy. Rare causes of NS include amyloidosis, immunoglobulin deposition disease, fibronectin glomerulopathy, and Collagenofibrotic glomerulopathy (CG). CG is caused by deposition of Type 3 collagen in the mesangium and subendothelial area. It usually presents as asymptomatic proteinuria, NS, hypertension, and renal failure. Histologically, it can present as Congo red-negative nodular glomerulosclerosis and requires electron microscopy for confirmation of diagnosis. Electron microscopy shows characteristic fibers which are curved, frayed and have a transverse band with periodicity of 43–65 nm. There is no specific treatment, and it can recur after kidney transplantation.


[FULL TEXT] [PDF]*
Print this article  Email this article
    

  Similar in PUBMED
    Search Pubmed for
    Search in Google Scholar for
   Citation Manager
  Access Statistics
   Reader Comments
   Email Alert *
   Add to My List *
 * Requires registration (Free)
 

 Article Access Statistics
    Viewed918    
    Printed10    
    Emailed0    
    PDF Downloaded92    
    Comments [Add]    

Recommend this journal